- - Mysteries Solved with Mysteries Solved with Radiology Radiology Dorothy Bulas M.D. David Kushner M.D. Childrens National Medical Center George Washington University No disclosures by the authors Objectives Understand indications for imaging studies Ultrasound CT/MRI Nuclear Medicine Order appropriate radiologic work up for Common diagnostic disorders Imaging issues Radiation exposure Sedation risk Cost Discomfort Fluoroscopy Pro No sedation Indications GI - malrotation, vascular rings, IBD, ulcers,Hirsprung, strictures, aspiration GU- Reflux, posterior urethral valves, neurogenic bladder Fluoroscopy Con Radiation exposure Discomfort from catheterizations, nausea Transportation Temperature control NPO for GI studies Ultrasound Pro No radiation Portable No sedation Inexpensive Ultrasound Indications Masses/abscesses Cranial- neonate, TCD for SSD GI- pyloric stenosis, IBD, AP, biliary GU- anatomy, Doppler, masses Vascular- thrombi,stenosis,AVM Extremities - hips,effusions Ultrasound Con Small field of view Crying, rapid breathing, gas, obesity limits resolution Limited resolution of solid organ lesions Technique dependent CT Scan Pro Large field of view Reproducible measurements 3D reconstruction Vascular characteristics CT Scan Indications Tumor staging and measurements Reproducible Lung, solid organ parenchymal lesions well visualized Vascular anatomy Interloop abscess/bowel Obese patients CT Scan Con Radiation exposure!! Possible sedation, NPO Oral contrast 2- 4 hours IV contrast- renal status, allergy hx Transport issues, temperature control Expense MRI Pro Exquisite detail Vascular characteristics-MRA/MRV Large field of view Multiple planes, 3D reconstruction Spectroscopy Cardiac physiology MRI Indications Cranial/spine anatomy Cardiac physiology Solid Tumors Infection - osteomyelitis/septic joint AVM Fetal anomalies MRI Con Expensive Long examination, sensitive to respiratory and cardiac motion Availability Transport, temperature control Sedation, NPO + IV access Angiography Pro Precise anatomy Therapeutic Indications Cranial- vasculitis, aneurysm, AMV Renal- vascular stenosis Pulmonary- embolization Angiography Con Invasive- hematoma, stroke risk Contrast - renal function,allergy Sedation Transportation Temperature control Radiation exposure Nuclear Medicine Pro Physiologic information Quantitative information Therapeutic Radiation may be less than fluoroscopy Fusion PET/CT may improve resolution Nuclear Medicine Indication Tumors- lymphoma,osteosarcoma, NB Infection- osteomyelitis Renal- reflux, function, obstruction Hepatobiliary- function, obstruction Meckels Milk scan Thyroid Nuclear Medicine Con Radiation exposure IV access May require sedation Poor resolution without fusion imaging Case 1 year old with unexplained burn Nonaccidental Trauma Skeletal survey oblique for rib fractures metaphyseal fractures Cranial CT / MRI Subdural hematomas Abdominal CT solid organ injuries Bone scan- good for confirmation, rib fxs or FU skeletal survey after 2 weeks Case 4 month old with stridor STRIDOR Croup Epiglottitis Vascular Rings Foreign Body Retropharyngeal Abscess Croup Subglottic narrowing Steeple sign Ballooned hypopharynx Epiglotitis Thumb sign Thick aryepiglottic folds Ballooned hypopharynx Retropharyngeal Abscess Infection/laceration Xray- prevertebral soft tissue swelling Fluoro CT with contrast STRIDOR Foreign Body Cough/wheeze Inlet/Carina/GE junction Xray insp/exp or decub Esophogram Vascular Rings Aberrant branching of the aortic arch Double arch/ Aberrant left subclavian Rt Aortic arch/ Pulmonary Sling Compress trachea/esophagus Diagnose by Barium swallow Echo/ CT/ MRI Neck Mass Lymphoma-CT Abscess-CT Brachial cleft cyst- US,CT,MR Thyroglossal duct cyst- US,CT,MR Thyroid- nodule,Hashimoto thyroiditis, papillary carcinoma- US, nuclear thyroid scan Case 2 week old with bilious vomiting Malrotation with Volvulus Clinical Presentation Bilious vomiting < 1 month in 80% Bloody Stool Abdominal distention Surgical Emergency Neonatal intestinal obstruction plain radiographs complete proximal obstruction incomplete obstruction complete distal obstruction contrast studies Case Newborn with failure to pass meconium Complete distal obstruction jejunal atresia meconium plug Hirschsprung small left colon contrast enema Normal colon Microcolon Ileal atresia meconium ileus total aganglionosis Meconium Ileus Radiologic Features Meconium peritonitis obstruction Contrast Enema Microcolon Meconium plugs in terminal ileum Therapeutic Hirschsprung Disease Absence of myenteric plexus cells (aganglionosis) of distal colon Male:female 6:1 Present with obstruction, constipation Complications of perforation, peritonitis Dx: rectal biopsy Hirschsprung Disease Enema can be normal in neonates Transition zone between normal and stenotic segment Hirschsprung disease Barium retention over 24 hours Case 6 week old with nonbilious vomiting Hypertrophic Pyloric Stenosis Hypertrophy of pyloric muscle 80% male, commonly first born 2 weeks - 4 months of age Caffeys,1993 Hypertrophic Pyloric Stenosis Nonbilious projectile vomiting Dehydration/alkalosis Weight loss Palpable olive RUQ Hypertrophic Pyloric Stenosis UGI String, shoulder, beak and tit signs Hypertrophic Pyloric Stenosis US evaluation Thick antropyloric muscle >3.5 mm most accurate Elongated pylorus Channel length >17 mm Case 5 year old with 3 episodes of painless rectal bleeding. Meckel Diverticulum Omphalomesenteric/vitteline duct remnant open at ileal end 15% ectopic gastric mucosa 4% of population Within 2 feet of ileocecal valve Most asymptomatic, 2% complications intussusception,volvulus,hemorrhage Meckels Diverticulum May present with ulceration/hemorrhage Obstruction from intussusception, volvulus, diverticulits Tc-99m pertechnetate scan Uptake by chief cells of ectopic gastric mucosa Accumulation in right midabdomen or right lower quadrant. Case 5 year old with right lower quadrant pain Appendicitis Most common cause of abdominal surgery in children Nausea/vomiting, anorexia, fever 30-45% atypical presentation retrocecal,pelvic, perforated perforation rate as high as 60% in children Rare in infants, increase frequency w/ each yr of childhood Appendicitis Radiographs fecolith 10-15% RLQ mass, SBO, scoliosis Appendicitis US Evaluation Graded compression (Puylaert, Rad 1986) Appendicitis if Noncompressible >6 mm appendecolith (30%) Look for extraluminal collections Exclude alternative diagnosis torsion, PID, intussusception, mesenteric adenitis . CT if patient large difficult to examine planning drainage intervention Case 2 year old with intermittent colicky abdominal pain. Intussusception Peak 5-9 months of age (75%) Colicky pain, vomiting, abdominal mass Currant jelly stools >90% lymphoid hyperplasia Pathologic lead point often in children> 4 yrs must rule out Meckels diverticulum, polyp, duplication, lymphoma Pathologic lead point often in children> 4 yrs - must rule out Meckels diverticulum, polyp, duplication, lymphoma Intussusception Radiologic Features XR -RUQ mass, air crescent sign, SBO US -Pseudokidney, target signs Enema Contraindicated if peritonitis, perforation or septic shock Surgical consult exclude free air IV Case 12 year old with weight loss, diarrhea Inflammatory Bowel Disease 25% present prior to age 20 Crohns:Ulcerative Colitis 2:1 Abdominal pain, diarrhea, rectal bleeding Inflammatory Bowel Disease Crohns Disease - entire thickness, skip areas, small bowel 50% Terminal ileum most common site gastric aphthous ulcers Ulcerative Colitis-mucosa/ submucosa rectum proximally without skip areas Inflammatory Bowel Disease Evaluation UGI for terminal ileum, fistula evaluation BE for colonic mucosal evaluation Inflammatory Bowel Disease Evaluation CT for interloop abscess, bowel thickening Colonoscopy for biopsy Case 3 year old with palpable abdominal mass Abdominal Mass AXR- R/O stool, calcifications, bowel obstruction US- R/O UPJ obstruction, helps plan for CT/MR CT for tumor staging Abdominal Mass CT- IV and oral contrast MRI- 3 plane imaging- useful for hepatic lesions, spinal cord involvement Neonatal Abdominal Mass 55%Renal UPJ, MCDK, RVT, IPKD 15% Gyn - ovarian cyst, dermoid 15% GI- duplication, mesenteric cyst 10% Retroperitoneal neuroblastoma, adrenal hemorrhage 5% Hepatobiliary hemangioendothelioma, mesenteric hamartoma, choledocal cyst, Pediatric Masses Renal (50%) Wilms, UPJ, IPKD Retroperitoneal (25%) NB,Teratoma,Lymphoma, rhabdo GI(20%) AP,intus,mes cyst, duplication,chol cyst Gyn-(5%) Ovarian cyst,torsion, hydrometrocopolpos Case 5 year old female with urinary tract infection and fever Renal Work up US- Anatomy hydronephrosis, duplex, ureterocele, VCUG /cystogram- reflux, PUV, neurogenic bladder CT- abscess, renal calculi, tumors Renal Work up Renal Lasix Scan- obstruction- UPJ,UPJ,PUV DMSA- UTI - scarring Case 13 year old female with pelvic pain GYN-Pelvic Pain US PID, TOA, Ectopic Ovarian Cyst, hemorrhagic cyst, torsion Dermoid Hydrometrocolpos Case 3 year old with limp Limping Child Toxic synovitis Septic arthritis Osteomyelitis Discitis SCFE Legg Perthes/AVN DDH Tumor Occult fracture Limping Child Xray US- Bone Scan- MRI- Osteomyelitis XR- 10-14 days periosteal reaction, lytic sclerotic lesions Bone scan metaphyseal MRI- for complications abscess myositis Case Two week old with hip click DDH Screen those at risk- breech, Equinovarus deformity (forefoot and hind foot varus), family history Hip click US 4-6 weeks of age FU monthly CT/MRI in spica cast Hip Evaluation STOP No risk factors US 4 wks Risk factors Normal Exam US 4 wks Stable Click Us 1-2 wks Unstable Click Abnormal Exam Clinical Exam