Beruflich Dokumente
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OLEH : CINTYA DUNIHAPSARI 012116354
PEMBIMBING : DR. OKTINA RACHMI DACHLIA, SP. RAD
MULTI-MODALITY IMAGING
REVIEW OF CONGENITAL
ABNORMALITIES OF KIDNEY
AND UPPER URINARY TRACT
Subraminayan Ramanathan, Devendra Kumar, Maneesh Khanna,
Mahmoud Al Heidous, Adnan Sheikh, Vivek Virmani, Yegu Palaniappan
RENAL CONGENITAL
ABNORMALITY
RELEVANT
EMBRYOLOGY
CLASSIFICATIO
N
CLINICAL PRESENTATION
AND IMAGING APPROACH
RELEVANT EMBRYOLOGI
RENAL CONGENITAL
ABNORMALITY
RENAL
PARENCHYME
MALFORMATION
ABNORMAL
MIGRATION
ABNORMAL
COLLECTING
SYSTEM
RENAL PARENCHYMAL
MALFORMARTION
ANOMALIES
IN NUMBER
ANOMALIES
IN SHAPE
PERSISTENT
PERSISTENT FETAL
FETAL LOBULATIONS
LOBULATIONS
RENAL
AGENESIS
HYPERTROPHIED
HYPERTROPHIED COLUMN
COLUMN OF
OF BERTINI
BERTINI
DROMUDARY
DROMUDARY HUMP
HUMP
RENAL
RENAL HILAR
HILAR LIP
LIP
SUPERNUMARY
KIDNEYS
JUNCTIONAL
JUNCTIONAL PARENCHYMAL
PARENCHYMAL DEFECT
DEFECT
RENAL
RENAL HYPOPLASIA
HYPOPLASIA
RENAL
RENAL DISPLASIA
DISPLASIA
ABNORMAL MIGRATION
ECTOPIC
KIDNEY
SIMPLE
CROSSHEAD
HORSESHOE
KIDNEY
ABNORMAL COLLECTING
SYSTEM
DUPLEX
COLLECTING
SYSTEM
CLINICAL PRESENTATION
AND IMAGING APPROACH
Antenatal Screening Ultrasonography (USG)
Detect early from second trimester
Ass : presence, location, size, structure and
echogenicity
Abnormality detected : hydronephrosis,
hydroureter, thickened bladder, cystic kidney,
small or dysplastic kidney and absent kidney
When to examine? soon after birth and
again at 4-6 week of age.
CLINICAL PRESENTATION
AND IMAGING APPROACH
Cross Sectional Imaging CT scan
Help in resolving the complex anatomy, ectopic
kidneys not detected on USG.
Useful for observe in duplex system
MRI
Lack of ionizing radiation
Better soft tissue contrast
Disadvantage : sedation in small children, cost
and availability
RENAL AGENESIS
RENAL AGENESIS
Coron
al
RENAL AGENESIS
Axi
al
RENAL AGENESIS
Absent Left
kidney
Left Seminal
Vesicle Cyst
BILATERAL RENAL
AGENESIS
SUPERNUMARY KIDNEY
SUPERNUMARY KIDNEYS
SOME RENAL
ANOMALIES IN SHAPE
PERSISTENT FETAL
LOBULATIONS
HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertin
HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertini
Coro
nal
Axial
HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertini
Coro
nal
Sagit
al
Dromedary Hump
Bul
ge
RENAL HYPOPLASIA
RENAL HYPOPLASIA
Renal
Hypoplasia
Coro
nal
Axial
RENAL DYSPLASIA
Normal Kidney
Multiple noncommunicating
cysts
ECTOPIC KIDNEYS
ECTOPIC KIDNEYS
Empty Renal
Fossa
Crossed ectopia
without fussion
ECTOPIC KIDNEYS
Crossed fused
ectopia
HORSESHOE KIDNEY
HORSESHOE KIDNEY
HORSESHOE KIDNEY
Ureteric
Stricture
Bifid Renal
Pelvis
Y Shaped
Ureter
V Shaped
Ureter
PUJO
PUJO
Hydronephr
osis
Coro
nal
PUJO
Axial
PUJO
a ka
sih
Terim
Tha
aaaa
nnk
youu
u :*