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JOURNAL

READING
OLEH : CINTYA DUNIHAPSARI 012116354
PEMBIMBING : DR. OKTINA RACHMI DACHLIA, SP. RAD

KEPANITERAAN KLINIK BAGIAN ILMU RADIOLOGI


RUMAH SAKIT DAERAH KOTA SEMARANG
FAKULTAS KEDOKTERAN UNIVERSITAS ISLAM SULTAN AGUNG
SEMARANG

MULTI-MODALITY IMAGING
REVIEW OF CONGENITAL
ABNORMALITIES OF KIDNEY
AND UPPER URINARY TRACT
Subraminayan Ramanathan, Devendra Kumar, Maneesh Khanna,
Mahmoud Al Heidous, Adnan Sheikh, Vivek Virmani, Yegu Palaniappan

RENAL CONGENITAL
ABNORMALITY
RELEVANT
EMBRYOLOGY
CLASSIFICATIO
N
CLINICAL PRESENTATION
AND IMAGING APPROACH

RELEVANT EMBRYOLOGI

RENAL CONGENITAL
ABNORMALITY

RENAL
PARENCHYME
MALFORMATION

ABNORMAL
MIGRATION

ABNORMAL
COLLECTING
SYSTEM

RENAL PARENCHYMAL
MALFORMARTION

ANOMALIES
IN NUMBER

ANOMALIES
IN SHAPE
PERSISTENT
PERSISTENT FETAL
FETAL LOBULATIONS
LOBULATIONS

RENAL
AGENESIS

HYPERTROPHIED
HYPERTROPHIED COLUMN
COLUMN OF
OF BERTINI
BERTINI
DROMUDARY
DROMUDARY HUMP
HUMP
RENAL
RENAL HILAR
HILAR LIP
LIP

SUPERNUMARY
KIDNEYS

JUNCTIONAL
JUNCTIONAL PARENCHYMAL
PARENCHYMAL DEFECT
DEFECT
RENAL
RENAL HYPOPLASIA
HYPOPLASIA
RENAL
RENAL DISPLASIA
DISPLASIA

ABNORMAL MIGRATION
ECTOPIC
KIDNEY

SIMPLE

CROSSHEAD

HORSESHOE
KIDNEY

ABNORMAL COLLECTING
SYSTEM
DUPLEX
COLLECTING
SYSTEM

PUJO / Pelvic Uretero


Junction Obstruction

CLINICAL PRESENTATION
AND IMAGING APPROACH
Antenatal Screening Ultrasonography (USG)
Detect early from second trimester
Ass : presence, location, size, structure and
echogenicity
Abnormality detected : hydronephrosis,
hydroureter, thickened bladder, cystic kidney,
small or dysplastic kidney and absent kidney
When to examine? soon after birth and
again at 4-6 week of age.

CLINICAL PRESENTATION
AND IMAGING APPROACH
Cross Sectional Imaging CT scan
Help in resolving the complex anatomy, ectopic
kidneys not detected on USG.
Useful for observe in duplex system
MRI
Lack of ionizing radiation
Better soft tissue contrast
Disadvantage : sedation in small children, cost
and availability

RENAL AGENESIS

RENAL AGENESIS

Coron
al

RENAL AGENESIS

Axi
al

RENAL AGENESIS
Absent Left
kidney

Left Seminal
Vesicle Cyst

BILATERAL RENAL
AGENESIS

SUPERNUMARY KIDNEY

SUPERNUMARY KIDNEYS

SOME RENAL
ANOMALIES IN SHAPE

PERSISTENT FETAL
LOBULATIONS

HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertin

HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertini

Coro
nal

Axial

HYPERTROPHIED COLUMN
BERTINI
Hipertrophied
Column of Bertini

Coro
nal

Sagit
al

Dromedary Hump

Bul
ge

RENAL HYPOPLASIA

RENAL HYPOPLASIA
Renal
Hypoplasia

Coro
nal

Axial

RENAL DYSPLASIA

Normal Kidney

Multiple noncommunicating
cysts

ECTOPIC KIDNEYS

ECTOPIC KIDNEYS
Empty Renal
Fossa

Crossed ectopia
without fussion

ECTOPIC KIDNEYS
Crossed fused
ectopia

HORSESHOE KIDNEY

HORSESHOE KIDNEY

HORSESHOE KIDNEY

DUPLEX COLLECTING SYSTEM

Ureteric
Stricture

Bifid Renal
Pelvis

Y Shaped
Ureter

V Shaped
Ureter

PUJO / PELVI URETERIC


JUNCTION OBSTRUCTION

PUJO

PUJO

Hydronephr
osis

Coro
nal

PUJO

Axial

PUJO

a ka
sih
Terim

Tha

aaaa

nnk
youu
u :*

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